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Frontiers of Targeted Therapy and Predictors of Treatment Response in Systemic Sclerosis

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heat shock protein 90; systemic sclerosis; established dermal fibrosis; treatment; pathogenesis; epigenetic mechanisms; miRNAs; calcinosis cutis; bisphosphonates; pamidronate; autoimmune connective tissue diseases; dermatomyositis; immune cells; anti-inflammatory; therapy; fibrosis; interleukin-6; Tocilizumab; pulmonary fibrosis; interstitial lung disease; progressive fibrosing interstitial lung disease; lung function; body mass index; clinical trial; metabolomics; LC-MS/MS; ion mobility; kynurenine pathway; urea cycle; lipids; gut dysbiosis; pulmonary arterial hypertension (PAH); biomarkers; miRNA; complement; myofibroblasts; macitentan; cough; pulmonary hypertension; predictors of treatment response; autoreactive B cells; autoantibodies; rituximab; aptamers; Seldeg; n/a; mixed connective tissue disease; systemic lupus erythematosus; Sjögren’s syndrome; rheumatoid arthritis; idiopathic inflammatory myopathy; national delphi consensus

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